Ehlers-Danlos syndrome (EDS) is a group of inherited connective tissue diseases that have in common a defect in collagen structure or synthesis. 

There are a number of variants with different modes of inheritance. 

• Kyphoscoliotic EDS: autosomal recessive form
• Vascular variant EDS: autosomal dominant form that causes rupture of vessels and bowel wall
• Classical EDS: autosomal dominant form that causes a type V collagen defect; patients have a normal lifespan 

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